Other congenital anomalies of upper alimentary tract


750       Other congenital anomalies of upper alimentary tract     (ICD 9 CM Codes)
Excludes:    dentofacial anomalies (524.0-524.9)
750.0    Tongue tie
Ankyloglossia
750.1    Other anomalies of tongue
750.10  Anomaly of tongue, unspecified
750.11  Aglossia
750.12  Congenital adhesions of tongue
750.13  Fissure of tongue
Bifid tongue
Double tongue
750.15  Macroglossia
Congenital hypertrophy of tongue
750.16  Microglossia
Hypoplasia of tongue
750.19  Other
750.2    Other specified anomalies of mouth and pharynx
750.21  Absence of salivary gland
750.22  Accessory salivary gland
750.23  Atresia, salivary gland
Imperforate salivary duct
750.24  Congenital fistula of salivary gland
750.25  Congenital fistula of lip
Congenital (mucus) lip pits
750.26  Other specified anomalies of mouth
Absence of uvula
750.27  Diverticulum of pharynx
Pharyngeal pouch
750.29  Other specified anomalies of pharynx
Imperforate pharynx
750.3    Tracheoesophageal fistula, esophageal atresia and stenosis
Absent esophagus
Atresia of esophagus
Congenital:
esophageal ring
stenosis of esophagus
stricture of esophagus
Congenital fistula:
esophagobronchial
esophagotracheal
Imperforate esophagus
Webbed esophagus
750.4    Other specified anomalies of esophagus
Dilatation, congenital, of esophagus
Displacement, congenital, of esophagus
Diverticulum of esophagus
Duplication of esophagus
Giant esophagus
Esophageal pouch
Excludes: congenital hiatus hernia (750.6)
750.5    Congenital hypertrophic pyloric stenosis
Congenital or infantile:
constriction of pylorus
hypertrophy of pylorus
spasm of pylorus
stenosis of pylorus
stricture of pylorus
750.6    Congenital hiatus hernia
Displacement of cardia through esophageal hiatus
Excludes: congenital diaphragmatic hernia (756.6)
750.7    Other specified anomalies of stomach
Congenital:
cardiospasm
hourglass stomach
Displacement of stomach
Diverticulum of stomach, congenital
Duplication of stomach
Megalogastria
Microgastria
Transposition of stomach
750.8    Other specified anomalies of upper alimentary tract
750.9    Unspecified anomaly of upper alimentary tract
Congenital:
anomaly NOS of upper alimentary tract [any part, except tongue]
deformity NOS of upper alimentary tract [any part, except tongue]
751       Other congenital anomalies of digestive system         (ICD 9 CM Codes)
751.0    Meckel's diverticulum
Meckel's diverticulum (displaced) (hypertrophic)
Persistent:
omphalomesenteric duct
vitelline duct
751.1    Atresia and stenosis of small intestine
Atresia of:
duodenum
ileum
intestine NOS
Congenital:
absence of small intestine or intestine NOS
obstruction of small intestine or intestine NOS
stenosis of small intestine or intestine NOS
stricture of small intestine or intestine NOS
Imperforate jejunum
751.2    Atresia and stenosis of large intestine, rectum, and anal canal
Absence:
anus (congenital)
appendix, congenital
large intestine, congenital
rectum
Atresia of:
anus
colon
rectum
Congenital or infantile:
obstruction of large intestine
occlusion of anus
stricture of anus
Imperforate:
anus
rectum
Stricture of rectum, congenital
751.3    Hirschsprung's disease and other congenital functional disorders of colon
Aganglionosis
Congenital dilation of colon
Congenital megacolon
Macrocolon
751.4    Anomalies of intestinal fixation
Congenital adhesions:
omental, anomalous
peritoneal
Jackson's membrane
Malrotation of colon
Rotation of cecum or colon:
failure of
incomplete
insufficient
Universal mesentery
751.5    Other anomalies of intestine
Congenital diverticulum, colon
Dolichocolon
Duplication of:
anus
appendix
cecum
intestine
Ectopic anus
Megaloappendix
Megaloduodenum
Microcolon
Persistent cloaca
Transposition of:
appendix
colon
intestine
751.6    Anomalies of gallbladder, bile ducts, and liver
751.60  Unspecified anomaly of gallbladder, bile ducts, and liver
751.61  Biliary atresia
Congenital:
absence of bile duct (common) or passage
hypoplasia of bile duct (common) or passage
obstruction of bile duct (common) or passage
stricture of bile duct (common) or passage
751.62  Congenital cystic disease of liver
Congenital polycystic disease of liver
Fibrocystic disease of liver
751.69  Other anomalies of gallbladder, bile ducts, and liver
Absence of:
gallbladder, congenital
liver (lobe)
Accessory:
hepatic ducts
liver
Congenital:
choledochal cyst
hepatomegaly
Duplication of:
biliary duct
cystic duct
gallbladder
liver
Floating:
gallbladder
liver
Intrahepatic gallbladder
751.7    Anomalies of pancreas
Absence of pancreas
Accessory pancreas
Agenesis of pancreas
Annular pancreas
Ectopic pancreatic tissue
Hypoplasia of pancreas
Pancreatic heterotopia
Excludes: diabetes mellitus (249.0-249.9, 250.0-250.9)
fibrocystic disease of pancreas (277.00-277.09)
neonatal diabetes mellitus (775.1)
751.8    Other specified anomalies of digestive system
Absence (complete) (partial) of alimentary tract NOS
Duplication of digestive organs NOS
Malposition, congenital of digestive organs NOS
Excludes: congenital diaphragmatic hernia (756.6)
congenital hiatus hernia (750.6)
751.9    Unspecified anomaly of digestive system
Congenital:
anomaly NOS of digestive system NOS
deformity NOS of digestive system NOS
752       Congenital anomalies of genital organs          (ICD 9 CM Codes)
Excludes:    syndromes associated with anomalies in the number and form of chromosomes (758.0-758.9)
752.0    Anomalies of ovaries
Absence, congenital, of ovary
Accessory ovary
Ectopic ovary
Streak of ovary
752.1    Anomalies of fallopian tubes and broad ligaments
752.10  Unspecified anomaly of fallopian tubes and broad ligaments
752.11  Embryonic cyst of fallopian tubes and broad ligaments
Cyst:
epoophoron
fimbrial
parovarian
752.19  Other
Absence of fallopian tube or broad ligament
Accessory fallopian tube or broad ligament
Atresia of fallopian tube or broad ligament
752.2    Doubling of uterus
Didelphic uterus
Doubling of uterus [any degree] (associated with doubling of cervix and vagina)
752.3    Other anomalies of uterus
752.31  Agenesis of uterus
Congenital absence of uterus
752.32  Hypoplasia of uterus
752.33  Unicornuate uterus
Unicornate uterus with or without a separate uterine horn
Uterus with only one functioning horn
752.34  Bicornuate uterus
Bicornuate uterus, complete or partial
752.35  Septate uterus
Septate uterus, complete or partial
752.36  Arcuate uterus
752.39  Other anomalies of uterus
Aplasia of uterus NOS
Müllerian anomaly of the uterus, NEC
Excludes: anomaly of uterus due to exposure to diethylstilbestrol [DES] in utero (760.76)
didelphic uterus (752.2)
doubling of uterus (752.2)
752.4    Anomalies of cervix, vagina, and external female genitalia
752.40  Unspecified anomaly of cervix, vagina, and external female genitalia
752.41  Embryonic cyst of cervix, vagina, and external female genitalia
Cyst of:
canal of Nuck, congenital
Gartner's duct
vagina, embryonal
vulva, congenital
752.42  Imperforate hymen
752.43  Cervical agenesis
Cervical hypoplasia
752.44  Cervical duplication
752.45  Vaginal agenesis
Agenesis of vagina, total or partial
752.46  Transverse vaginal septum
752.47  Longitudinal vaginal septum
Longitudinal vaginal septum with or without obstruction
752.49  Other anomalies of cervix, vagina, and external female genitalia
Absence of clitoris or vulva
Agenesis of clitoris or vulva
Anomalies of cervix, NEC
Anomalies of hymen, NEC
Congenital stenosis or stricture of:
cervical canal
vagina
Müllerian anomalies of the cervix and vagina, NEC
Excludes: double vagina associated with total duplication (752.2)
752.5    Undescended and retractile testicle
752.51  Undescended testis
Cryptorchism
Ectopic testis
752.52  Retractile testis
752.6    Hypospadias and epispadias and other penile anomalies
752.61  Hypospadias
752.62  Epispadias
Anaspadias
752.63  Congenital chordee
752.64  Micropenis
752.65  Hidden penis
752.69  Other penile anomalies
752.7    Indeterminate sex and pseudohermaphroditism
Gynandrism
Hermaphroditism
Ovotestis
Pseudohermaphroditism (male) (female)
Pure gonadal dysgenesis
Excludes: androgen insensitivity (259.50-259.52)
pseudohermaphroditism:
female, with adrenocortical disorder (255.2)
male, with gonadal disorder (257.8)
with specified chromosomal anomaly (758.0-758.9)
testicular feminization syndrome (259.50-259.52)
752.8    Other specified anomalies of genital organs
Excludes: congenital hydrocele (778.6)
penile anomalies (752.61-752.69)
phimosis or paraphimosis (605)
752.81  Scrotal transposition
752.89  Other specified anomalies of genital organs
Absence of:
prostate
spermatic cord
vas deferens
Anorchism
Aplasia (congenital) of:
prostate
round ligament
testicle
Atresia of:
ejaculatory duct
vas deferens
Fusion of testes
Hypoplasia of testis
Monorchism
Polyorchism
752.9    Unspecified anomaly of genital organs
Congenital:
anomaly NOS of genital organ, NEC
deformity NOS of genital organ, NEC
753       Congenital anomalies of urinary system              (ICD 9 CM Codes)
753.0    Renal agenesis and dysgenesis
Atrophy of kidney:
congenital
infantile
Congenital absence of kidney(s)
Hypoplasia of kidney(s)
753.1    Cystic kidney disease
Excludes: acquired cyst of kidney (593.2)
753.10  Cystic kidney disease, unspecified
753.11  Congenital single renal cyst
753.12  Polycystic kidney, unspecified type
753.13  Polycystic kidney, autosomal dominant
753.14  Polycystic kidney, autosomal recessive
753.15  Renal dysplasia
753.16  Medullary cystic kidney
Nephronopthisis
753.17  Medullary sponge kidney
753.19  Other specified cystic kidney disease
Multicystic kidney
753.2    Obstructive defects of renal pelvis and ureter
753.20  Unspecified obstructive defect of renal pelvis and ureter
753.21  Congenital obstruction of ureteropelvic junction
753.22  Congenital obstruction of ureterovesical junction
Adynamic ureter
Congenital hydroureter
753.23  Congenital ureterocele
753.29  Other
753.3    Other specified anomalies of kidney
Accessory kidney
Congenital:
calculus of kidney
displaced kidney
Discoid kidney
Double kidney with double pelvis
Ectopic kidney
Fusion of kidneys
Giant kidney
Horseshoe kidney
Hyperplasia of kidney
Lobulation of kidney
Malrotation of kidney
Trifid kidney (pelvis)
753.4    Other specified anomalies of ureter
Absent ureter
Accessory ureter
Deviation of ureter
Displaced ureteric orifice
Double ureter
Ectopic ureter
Implantation, anomalous, of ureter
753.5    Exstrophy of urinary bladder
Ectopia vesicae
Extroversion of bladder
753.6    Atresia and stenosis of urethra and bladder neck
Congenital obstruction:
bladder neck
urethra
Congenital stricture of:
urethra (valvular)
urinary meatus
vesicourethral orifice
Imperforate urinary meatus
Impervious urethra
Urethral valve formation
753.7    Anomalies of urachus
Cyst (of) urachus
Fistula (of) urachus
Patent (of) urachus
Persistent umbilical sinus
753.8    Other specified anomalies of bladder and urethra
Absence, congenital of:
bladder
urethra
Accessory:
bladder
urethra
Congenital:
diverticulum of bladder
hernia of bladder
Congenital urethrorectal fistula
Congenital prolapse of:
bladder (mucosa)
urethra
Double:
urethra
urinary meatus
753.9    Unspecified anomaly of urinary system
Congenital:
anomaly NOS of urinary system [any part, except urachus]
deformity NOS  of urinary system [any part, except urachus]
754       Certain congenital musculoskeletal deformities           (ICD 9 CM Codes)
Includes:     nonteratogenic deformities which are considered to be due to intrauterine malposition and pressure
754.0    Of skull, face, and jaw
Asymmetry of face
Compression facies
Depressions in skull
Deviation of nasal septum, congenital
Dolichocephaly
Plagiocephaly
Potter's facies
Squashed or bent nose, congenital
Excludes: dentofacial anomalies (524.0-524.9)
syphilitic saddle nose (090.5)
754.1    Of sternocleidomastoid muscle
Congenital sternomastoid torticollis
Congenital wryneck
Contracture of sternocleidomastoid (muscle)
Sternomastoid tumor
754.2    Of spine
Congenital postural:
lordosis
scoliosis
754.3    Congenital dislocation of hip
754.30  Congenital dislocation of hip, unilateral
Congenital dislocation of hip NOS
754.31  Congenital dislocation of hip, bilateral
754.32  Congenital subluxation of hip, unilateral
Congenital flexion deformity, hip or thigh
Predislocation status of hip at birth
Preluxation of hip, congenital
754.33  Congenital subluxation of hip, bilateral
754.35  Congenital dislocation of one hip with subluxation of other hip
754.4    Congenital genu recurvatum and bowing of long bones of leg
754.40  Genu recurvatum
754.41  Congenital dislocation of knee (with genu recurvatum)
754.42  Congenital bowing of femur
754.43  Congenital bowing of tibia and fibula
754.44  Congenital bowing of unspecified long bones of leg
754.5    Varus deformities of feet
Excludes: acquired (736.71, 736.75, 736.79)
754.50  Talipes varus
Congenital varus deformity of foot, unspecified
Pes varus
754.51  Talipes equinovarus
Equinovarus (congenital)
754.52  Metatarsus primus varus
754.53  Metatarsus varus
754.59  Other
Talipes calcaneovarus
754.6    Valgus deformities of feet
Excludes: valgus deformity of foot (acquired) (736.79)
754.60  Talipes valgus
Congenital valgus deformity of foot, unspecified
754.61  Congenital pes planus
Congenital rocker bottom flat foot
Flat foot, congenital
Excludes: pes planus (acquired) (734)
754.62  Talipes calcaneovalgus
754.69  Other
Talipes:
equinovalgus
planovalgus
754.7    Other deformities of feet
Excludes: acquired (736.70-736.79)
754.70  Talipes, unspecified
Congenital deformity of foot NOS
754.71  Talipes cavus
Cavus foot (congenital)
754.79  Other
Asymmetric talipes
Talipes:
calcaneus
equinus
754.8    Other specified nonteratogenic anomalies
754.81  Pectus excavatum
Congenital funnel chest
754.82  Pectus carinatum
Congenital pigeon chest [breast]
754.89  Other
Club hand (congenital)
Congenital:
deformity of chest wall
dislocation of elbow
Generalized flexion contractures of lower limb joints, congenital
Spade-like hand (congenital)
755       Other congenital anomalies of limbs                   (ICD 9 CM Codes)
Excludes:    those deformities classifiable to 754.0-754.8
755.0    Polydactyly
755.00  Polydactyly, unspecified digits
Supernumerary digits
755.01  Of fingers
Accessory fingers
755.02  Of toes
Accessory toes
755.1    Syndactyly
Symphalangy
Webbing of digits
755.10  Of multiple and unspecified sites
755.11  Of fingers without fusion of bone
755.12  Of fingers with fusion of bone
755.13  Of toes without fusion of bone
755.14  Of toes with fusion of bone
755.2    Reduction deformities of upper limb
755.20  Unspecified reduction deformity of upper limb
Ectromelia NOS of upper limb
Hemimelia NOS of upper limb
Shortening of arm, congenital
755.21  Transverse deficiency of upper limb
Amelia of upper limb
Congenital absence of:
fingers, all (complete or partial)
forearm, including hand and fingers
upper limb, complete
Congenital amputation of upper limb
Transverse hemimelia of upper limb
755.22  Longitudinal deficiency of upper limb, NEC
Phocomelia NOS of upper limb
Rudimentary arm
755.23  Longitudinal deficiency, combined, involving humerus, radius, and ulna (complete or incomplete)
Congenital absence of arm and forearm (complete or incomplete) with or without metacarpal deficiency and/or phalangeal deficiency, incomplete
Phocomelia, complete, of upper limb
755.24  Longitudinal deficiency, humeral, complete or partial (with or without distal deficiencies, incomplete)
Congenital absence of humerus (with or without absence of some [but not all] distal elements)
Proximal phocomelia of upper limb
755.25  Longitudinal deficiency, radioulnar, complete or partial (with or without distal deficiencies, incomplete)
Congenital absence of radius and ulna (with or without absence of some [but not all] distal elements)
Distal phocomelia of upper limb
755.26  Longitudinal deficiency, radial, complete or partial (with or without distal deficiencies, incomplete)
Agenesis of radius
Congenital absence of radius (with or without absence of some [but not all] distal elements)
755.27  Longitudinal deficiency, ulnar, complete or partial (with or without distal deficiencies, incomplete)
Agenesis of ulna
Congenital absence of ulna (with or without absence of some [but not all] distal elements)
755.28  Longitudinal deficiency, carpals or metacarpals, complete or partial (with or without incomplete phalangeal deficiency)
755.29  Longitudinal deficiency, phalanges, complete or partial
Absence of finger, congenital
Aphalangia of upper limb, terminal, complete or partial
Excludes: terminal deficiency of all five digits (755.21)
transverse deficiency of phalanges (755.21)
755.3    Reduction deformities of lower limb
755.30  Unspecified reduction deformity of lower limb
Ectromelia NOS of lower limb
Hemimelia NOS of lower limb
Shortening of leg, congenital
755.31  Transverse deficiency of lower limb
Amelia of lower limb
Congenital absence of:
foot
leg, including foot and toes
lower limb, complete
toes, all, complete
Transverse hemimelia of lower limb
755.32  Longitudinal deficiency of lower limb, NEC
Phocomelia NOS of lower limb
755.33  Longitudinal deficiency, combined, involving femur, tibia, and fibula (complete or incomplete)
Congenital absence of thigh and (lower) leg (complete or incomplete) with or without metacarpal deficiency and/or phalangeal deficiency, incomplete
Phocomelia, complete, of lower limb
755.34  Longitudinal deficiency, femoral, complete or partial (with or without distal deficiencies, incomplete)
Congenital absence of femur (with or without absence of some [but not all] distal elements)
Proximal phocomelia of lower limb
755.35  Longitudinal deficiency, tibiofibular, complete or partial (with or without distal deficiencies, incomplete)
Congenital absence of tibia and fibula (with or without absence of some [but not all] distal elements)
Distal phocomelia of lower limb
755.36  Longitudinal deficiency, tibia, complete or partial (with or without distal deficiencies, incomplete)
Agenesis of tibia
Congenital absence of tibia (with or without absence of some [but not all] distal elements)
755.37  Longitudinal deficiency, fibular, complete or partial (with or without distal deficiencies, incomplete)
Agenesis of fibula
Congenital absence of fibula (with or without absence of some [but not all] distal elements)
755.38  Longitudinal deficiency, tarsals or metatarsals, complete or partial (with or without incomplete phalangeal deficiency)
755.39  Longitudinal deficiency, phalanges, complete or partial
Absence of toe, congenital
Aphalangia of lower limb, terminal, complete or partial
Excludes: terminal deficiency of all five digits (755.31)
transverse deficiency of phalanges (755.31)
755.4    Reduction deformities, unspecified limb
Absence, congenital (complete or partial) of limb NOS
Amelia of unspecified limb
Ectromelia of unspecified limb
Hemimelia of unspecified limb
Phocomelia of unspecified limb
755.5    Other anomalies of upper limb, including shoulder girdle
755.50  Unspecified anomaly of upper limb
755.51  Congenital deformity of clavicle
755.52  Congenital elevation of scapula
Sprengel's deformity
755.53  Radioulnar synostosis
755.54  Madelung's deformity
755.55  Acrocephalosyndactyly
Apert's syndrome
755.56  Accessory carpal bones
755.57  Macrodactylia (fingers)
755.58  Cleft hand, congenital
Lobster-claw hand
755.59  Other
Cleidocranial dysostosis
Cubitus:
valgus, congenital
varus, congenital
Excludes: club hand (congenital) (754.89)
congenital dislocation of elbow (754.89)
755.6    Other anomalies of lower limb, including pelvic girdle
755.60  Unspecified anomaly of lower limb
755.61  Coxa valga, congenital
755.62  Coxa vara, congenital
755.63  Other congenital deformity of hip (joint)
Congenital anteversion of femur (neck)
Excludes: congenital dislocation of hip (754.30-754.35)
755.64  Congenital deformity of knee (joint)
Congenital:
absence of patella
genu valgum [knock-knee]
genu varum [bowleg]
Rudimentary patella
755.65  Macrodactylia of toes
755.66  Other anomalies of toes
Congenital:
hallux valgus
hallux varus
hammer toe
755.67  Anomalies of foot, NEC
Astragaloscaphoid synostosis
Calcaneonavicular bar
Coalition of calcaneus
Talonavicular synostosis
Tarsal coalitions
755.69  Other
Congenital:
angulation of tibia
deformity (of):
ankle (joint)
sacroiliac (joint)
fusion of sacroiliac joint
755.8    Other specified anomalies of unspecified limb
755.9    Unspecified anomaly of unspecified limb
Congenital:
anomaly NOS of unspecified limb
deformity NOS of unspecified limb
Excludes: reduction deformity of unspecified limb (755.4)
756       Other congenital musculoskeletal anomalies              (ICD 9 CM Codes)
Excludes:    congenital myotonic chondrodystrophy (359.23)
those deformities classifiable to 754.0-754.8
756.0    Anomalies of skull and face bones
Absence of skull bones
Acrocephaly
Congenital deformity of forehead
Craniosynostosis
Crouzon's disease
Hypertelorism
Imperfect fusion of skull
Oxycephaly
Platybasia
Premature closure of cranial sutures
Tower skull
Trigonocephaly
Excludes: acrocephalosyndactyly [Apert's syndrome] (755.55)
dentofacial anomalies (524.0-524.9)
skull defects associated with brain anomalies, such as:
anencephalus (740.0)
encephalocele (742.0)
hydrocephalus (742.3)
microcephalus (742.1)
756.1    Anomalies of spine
756.10  Anomaly of spine, unspecified
756.11  Spondylolysis, lumbosacral region
Prespondylolisthesis (lumbosacral)
756.12  Spondylolisthesis
756.13  Absence of vertebra, congenital
756.14  Hemivertebra
756.15  Fusion of spine [vertebra], congenital
756.16  Klippel-Feil syndrome
756.17  Spina bifida occulta
Excludes: spina bifida (aperta) (741.0-741.9)
756.19  Other
Platyspondylia
Supernumerary vertebra
756.2    Cervical rib
Supernumerary rib in the cervical region
756.3    Other anomalies of ribs and sternum
Congenital absence of:
rib
sternum
Congenital:
fissure of sternum
fusion of ribs
Sternum bifidum
Excludes: nonteratogenic deformity of chest wall (754.81-754.89)
756.4    Chondrodystrophy
Achondroplasia
Chondrodystrophia (fetalis)
Dyschondroplasia
Enchondromatosis
Ollier's disease
Excludes: congenital myotonic chondrodystrophy (359.23)
lipochondrodystrophy [Hurler's syndrome] (277.5)
Morquio's disease (277.5)
756.5    Osteodystrophies
756.50  Osteodystrophy, unspecified
756.51  Osteogenesis imperfecta
Fragilitas ossium
Osteopsathyrosis
756.52  Osteopetrosis
756.53  Osteopoikilosis
756.54  Polyostotic fibrous dysplasia of bone
756.55  Chondroectodermal dysplasia
Ellis-van Creveld syndrome
756.56  Multiple epiphyseal dysplasia
756.59  Other
Albright (-McCune)-Sternberg syndrome
756.6    Anomalies of diaphragm
Absence of diaphragm
Congenital hernia:
diaphragmatic
foramen of Morgagni
Eventration of diaphragm
Excludes: congenital hiatus hernia (750.6)
756.7    Anomalies of abdominal wall
756.70  Anomaly of abdominal wall, unspecified
756.71  Prune belly syndrome
Eagle-Barrett syndrome
Prolapse of bladder mucosa
756.72  Omphalocele
Exomphalos
756.73  Gastroschisis
756.79  Other congenital anomalies of abdominal wall
Excludes: umbilical hernia (551-553 with.1)
756.8    Other specified anomalies of muscle, tendon, fascia, and connective tissue
756.81  Absence of muscle and tendon
Absence of muscle (pectoral)
756.82  Accessory muscle
756.83  Ehlers-Danlos syndrome
756.89  Other
Amyotrophia congenita
Congenital shortening of tendon
756.9    Other and unspecified anomalies of musculoskeletal system
Congenital:
anomaly NOS of musculoskeletal system, NEC
deformity NOS of musculoskeletal system, NEC
757       Congenital anomalies of the integument                 (ICD 9 CM Codes)
Includes:     anomalies of skin, subcutaneous tissue, hair, nails, and breast
Excludes:    hemangioma (228.00-228.09)
pigmented nevus (216.0-216.9)
757.0    Hereditary edema of legs
Congenital lymphedema
Hereditary trophedema
Milroy's disease
757.1    Ichthyosis congenita
Congenital ichthyosis
Harlequin fetus
Ichthyosiform erythroderma
757.2    Dermatoglyphic anomalies
Abnormal palmar creases
757.3    Other specified anomalies of skin
757.31  Congenital ectodermal dysplasia
757.32  Vascular hamartomas
Birthmarks
Port-wine stain
Strawberry nevus
757.33  Congenital pigmentary anomalies of skin
Congenital poikiloderma
Urticaria pigmentosa
Xeroderma pigmentosum
Excludes: albinism (270.2)
757.39  Other
Accessory skin tags, congenital
Congenital scar
Epidermolysis bullosa
Keratoderma (congenital)
Excludes: pilonidal cyst (685.0-685.1)
757.4    Specified anomalies of hair
Congenital:
alopecia
atrichosis
beaded hair
hypertrichosis
monilethrix
Persistent lanugo
757.5    Specified anomalies of nails
Anonychia
Congenital:
clubnail
koilonychia
leukonychia
onychauxis
pachyonychia
757.6    Specified congenital anomalies of breast
Accessory breast or nipple
Congenital absent breast or nipple
Supernumerary breast or nipple
Excludes: absence of pectoral muscle (756.81)
hypoplasia of breast (611.82)
micromastia (611.82)
757.8    Other specified anomalies of the integument
757.9    Unspecified anomaly of the integument
Congenital:
anomaly NOS of integument
deformity NOS of integument
758       Chromosomal anomalies                 (ICD 9 CM Codes)
Includes:     syndromes associated with anomalies in the number and form of chromosomes
Use additional codes for conditions associated with the chromosomal anomalies
758.0    Down's syndrome
Mongolism
Translocation Down's syndrome
Trisomy:
21 or 22
G
758.1    Patau's syndrome
Trisomy:
13
D1
758.2    Edward's syndrome
Trisomy:
18
E3
758.3    Autosomal deletion syndromes
758.31  Cri-du-chat syndrome
Deletion 5p
758.32  Velo-cardio-facial syndrome
Deletion 22q11.2
758.33  Other microdeletions
Miller-Dieker syndrome
Smith-Magenis syndrome
758.39  Other autosomal deletions
758.4    Balanced autosomal translocation in normal individual
758.5    Other conditions due to autosomal anomalies
Accessory autosomes NEC
758.6    Gonadal dysgenesis
Ovarian dysgenesis
Turner's syndrome
XO syndrome
Excludes: pure gonadal dysgenesis (752.7)
758.7    Klinefelter's syndrome
XXY syndrome
758.8    Other conditions due to chromosome anomalies
758.81  Other conditions due to sex chromosome anomalies
758.89  Other
758.9    Conditions due to anomaly of unspecified chromosome
759       Other and unspecified congenital anomalies         (ICD 9 CM Codes)
759.0    Anomalies of spleen
Aberrant spleen
Absent spleen
Accessory spleen
Congenital splenomegaly
Ectopic spleen
Lobulation of spleen
759.1    Anomalies of adrenal gland
Aberrant adrenal gland
Absent adrenal gland
Accessory adrenal gland
Excludes: adrenogenital disorders (255.2)
congenital disorders of steroid metabolism (255.2)
759.2    Anomalies of other endocrine glands
Absent parathyroid gland
Accessory thyroid gland
Persistent thyroglossal or thyrolingual duct
Thyroglossal (duct) cyst
Excludes: congenital:
goiter (246.1)
hypothyroidism (243)
759.3    Situs inversus
Situs inversus or transversus:
abdominalis
thoracis
Transposition of viscera:
abdominal
thoracic
Excludes: dextrocardia without mention of complete transposition (746.87)
759.4    Conjoined twins
Craniopagus
Dicephalus
Pygopagus
Thoracopagus
Xiphopagus
759.5    Tuberous sclerosis
Bourneville's disease
Epiloia
759.6    Other hamartoses, NEC
Syndrome:
Peutz-Jeghers
Sturge-Weber (-Dimitri)
von Hippel-Lindau
Excludes: neurofibromatosis (237.70-237.79)
759.7    Multiple congenital anomalies, so described
Congenital:
anomaly, multiple NOS
deformity, multiple NOS
759.8    Other specified anomalies
759.81  Prader-Willi syndrome
759.82  Marfan syndrome
759.83  Fragile X syndrome
759.89  Other
Congenital malformation syndromes affecting multiple systems, NEC
Laurence-Moon-Biedl syndrome
759.9    Congenital anomaly, unspecified

  (ICD 9 CM Codes)

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