Diseases Of The Blood And Blood-Forming Organs ICD 9 Codes (280-289)


4.  DISEASES OF THE BLOOD AND BLOOD-FORMING ORGANS (ICD 9 CODES: 280-289)
280       Iron deficiency anemias
Includes:     anemia:
asiderotic
hypochromic-microcytic
sideropenic
Excludes:    familial microcytic anemia (282.49)
280.0    Secondary to blood loss (chronic)
Normocytic anemia due to blood loss
Excludes: acute posthemorrhagic anemia (285.1)
280.1    Secondary to inadequate dietary iron intake
280.8    Other specified iron deficiency anemias
Paterson-Kelly syndrome
Plummer-Vinson syndrome
Sideropenic dysphagia
280.9    Iron deficiency anemia, unspecified
Anemia:
achlorhydric
chlorotic
idiopathic hypochromic
iron [Fe] deficiency NOS
281       Other deficiency anemias
281.0    Pernicious anemia
Anemia:
Addison's
Biermer's
congenital pernicious
Congenital intrinsic factor [Castle's] deficiency
Excludes: combined system disease without mention of anemia (266.2)
subacute degeneration of spinal cord without mention of anemia (266.2)
281.1    Other vitamin B12 deficiency anemia
Anemia:
vegan's
vitamin B12 deficiency (dietary)
due to selective vitamin B12 malabsorption with proteinuria
Syndrome:
Imerslund's
Imerslund-Gräsbeck
Excludes: combined system disease without mention of anemia (266.2)
subacute degeneration of spinal cord without mention of anemia (266.2)
281.2    Folate-deficiency anemia
Congenital folate malabsorption
Folate or folic acid deficiency anemia:
NOS
dietary
drug-induced
Goat's milk anemia
Nutritional megaloblastic anemia (of infancy)
Use additional E code to identify drug
281.3    Other specified megaloblastic anemias, not elsewhere classified
Combined B12 and folate-deficiency anemia
281.4    Protein-deficiency anemia
Amino-acid-deficiency anemia
281.8    Anemia associated with other specified nutritional deficiency
Scorbutic anemia
281.9    Unspecified deficiency anemia
Anemia:
dimorphic
macrocytic
megaloblastic NOS
nutritional NOS
simple chronic
282       Hereditary hemolytic anemias
282.0    Hereditary spherocytosis
Acholuric (familial) jaundice
Congenital hemolytic anemia (spherocytic)
Congenital spherocytosis
Minkowski-Chauffard syndrome
Spherocytosis (familial)
Excludes: hemolytic anemia of newborn (773.0-773.5)
282.1    Hereditary elliptocytosis
Elliptocytosis (congenital)
Ovalocytosis (congenital) (hereditary)
282.2    Anemias due to disorders of glutathione metabolism
Anemia:
6-phosphogluconic dehydrogenase deficiency
enzyme deficiency, drug-induced
erythrocytic glutathione deficiency
glucose-6-phosphate dehydrogenase [G-6-PD] deficiency
glutathione-reductase deficiency
hemolytic nonspherocytic (hereditary), type I
Disorder of pentose phosphate pathway
Favism
282.3    Other hemolytic anemias due to enzyme deficiency
Anemia:
hemolytic nonspherocytic (hereditary), type II
hexokinase deficiency
pyruvate kinase [PK] deficiency
triosephosphate isomerase deficiency
282.4    Thalassemias
Excludes: sickle-cell:
disease (282.60-282.69)
trait (282.5)
282.40  Thalassemia, unspecified
Thalassemia NOS
282.41  Sickle-cell thalassemia without crisis
Microdrepanocytosis
Sickle-cell thalassemia NOS
Thalassemia Hb-S disease without crisis
282.42  Sickle-cell thalassemia with crisis
Sickle-cell thalassemia with vaso-occlusive pain
Thalassemia Hb-S disease with crisis
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.43  Alpha thalassemia
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia
Excludes: alpha thalassemia trait or minor (282.46)
hydrops fetalis due to isoimmunization (773.3)
hydrops fetalis not due to immune hemolysis (778.0)
282.44  Beta thalassemia
Beta thalassemia major
Cooley's anemia
Homozygous beta thalassemia
Severe beta thalassemia
Thalassemia intermedia
Thalassemia major
Excludes: beta thalassemia minor (282.46)
beta thalassemia trait (282.46)
delta-beta thalassemia (282.45)
hemoglobin E beta thalassemia (282.47)
sickle-cell beta thalassemia (282.41, 282.42)
282.45  Delta-beta thalassemia
Homozygous delta-beta thalassemia
Excludes: delta-beta thalassemia trait (282.46)
282.46  Thalassemia minor
Alpha thalassemia minor
Alpha thalassemia silent carrier
Alpha thalassemia trait
Beta thalassemia minor
Beta thalassemia trait
Delta-beta thalassemia trait
Thalassemia trait NOS
Excludes: alpha thalassemia (282.43)
beta thalassemia (282.44)
delta-beta thalassemia (282.45)
hemoglobin E-beta thalassemia (282.47)
sickle-cell trait (282.5)
282.47  Hemoglobin E-beta thalassemia
Excludes: beta thalassemia (282.44)
beta thalassemia minor (282.46)
beta thalassemia trait (282.46)
delta-beta thalassemia (282.45)
delta-beta thalassemia trait (282.46)
hemoglobin E disease (282.7)
other hemoglobinopathies (282.7)
sickle-cell beta thalassemia (282.41, 282.42)
282.49  Other thalassemia
Dominant thalassemia
Hemoglobin C thalassemia
Hereditary leptocytosis
Mediterranean anemia (with other hemoglobinopathy)
Mixed thalassemia
Thalassemia with other hemoglobinopathy
Excludes: hemoglobin C disease (282.7)
hemoglobin E disease (282.7)
other hemoglobinopathies (282.7)
sickle-cell anemias (282.60-282.69)
sickle-cell beta thalassemia (282.41-282.42)
282.5    Sickle-cell trait
Hb-AS genotype
Hemoglobin S [Hb-S] trait
Heterozygous:
hemoglobin S
Hb-S
Excludes: that with other hemoglobinopathy (282.60-282.69)
that with thalassemia (282.41-282.42)
282.6    Sickle-cell disease
Sickle-cell anemia
Excludes: sickle-cell thalassemia (282.41-282.42)
sickle-cell trait (282.5)
282.60  Sickle-cell disease, unspecified
Sickle-cell anemia NOS
282.61  Hb-SS disease without crisis
282.62  Hb-SS disease with crisis
Hb-SS disease with vaso-occlusive pain
Sickle-cell crisis NOS
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.63  Sickle-cell/Hb-C disease without crisis
Hb-S/Hb-C disease without crisis
282.64  Sickle-cell/HB-C disease with crisis
Hb-S/Hb-C disease with crisis
Sickle-cell/Hb-C disease with vaso-occlusive pain
Use additional code for types of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.68  Other sickle-cell disease without crisis
Hb-S/Hb-D disease without crisis
Hb-S/Hb-E disease without crisis
Sickle-cell/Hb-D disease without crisis
Sickle-cell/Hb-E disease without crisis
282.69  Other sickle-cell disease with crisis
Hb-S/Hb-D disease with crisis
Hb-S/Hb-E disease with crisis
Sickle-cell/Hb-D disease with crisis
Sickle-cell/Hb-E disease with crisis
Other sickle-cell disease with vaso-occlusive pain
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.7    Other hemoglobinopathies
Abnormal hemoglobin NOS
Congenital Heinz-body anemia
Disease:
hemoglobin C [Hb-C]
hemoglobin D [Hb-D]
hemoglobin E [Hb-E]
hemoglobin Zurich [Hb-Zurich]
Hemoglobinopathy NOS
Hereditary persistence of fetal hemoglobin [HPFH]
Unstable hemoglobin hemolytic disease
Excludes: familial polycythemia (289.6)
hemoglobin E-beta thalassemia (282.47)
hemoglobin M [Hb-M] disease (289.7)
high-oxygen-affinity hemoglobin (289.0)
other hemoglobinopathies with thalassemia (282.49)
282.8    Other specified hereditary hemolytic anemias
Stomatocytosis
282.9    Hereditary hemolytic anemia, unspecified
Hereditary hemolytic anemia NOS
283       Acquired hemolytic anemias
283.0    Autoimmune hemolytic anemias
Autoimmune hemolytic disease (cold type) (warm type)
Chronic cold hemagglutinin disease
Cold agglutinin disease or hemoglobinuria
Hemolytic anemia:
cold type (secondary) (symptomatic)
drug-induced
warm type (secondary) (symptomatic)
Use additional E code to identify cause,  if drug-induced
Excludes: Evans' syndrome (287.32)
hemolytic disease of newborn (773.0-773.5)
283.1    Non-autoimmune hemolytic anemias
283.10  Non-autoimmune hemolytic anemia, unspecified
283.11  Hemolytic-uremic syndrome
Use additional code to identify associated:
E. coli infection (041.41-041.49)
Pneumococcal pnemonia (481)
Shigella dysenteriae (004.0)
283.19  Other non-autoimmune hemolytic anemias
Hemolytic anemia:
mechanical
microangiopathic
toxic
Use additional E code to identify cause
283.2    Hemoglobinuria due to hemolysis from external causes
Acute intravascular hemolysis
Hemoglobinuria:
from exertion
march
paroxysmal (cold) (nocturnal)
due to other hemolysis
Marchiafava-Micheli syndrome
Use additional E code to identify cause
283.9    Acquired hemolytic anemia, unspecified
Acquired hemolytic anemia NOS
Chronic idiopathic hemolytic anemia
284       Aplastic anemia and other bone marrow failure syndromes
284.0    Constitutional aplastic anemia
284.01  Constitutional red blood cell aplasia
Aplasia, (pure) red cell:
congenital
of infants
primary
Blackfan-Diamond syndrome
Familial hypoplastic anemia
284.09  Other constitutional aplastic anemia
Fanconi's anemia
Pancytopenia with malformations
284.1    Pancytopenia
Excludes: pancytopenia (due to) (with):
aplastic anemia NOS (284.9)
bone marrow infiltration (284.2)
constitutional red blood cell aplasia (284.01)
hairy cell leukemia (202.4)
human immunodeficiency virus disease (042)
leukoerythroblastic anemia (284.2)
malformations (284.09)
myelodysplastic syndromes (238.72-238.75)
myeloproliferative disease (238.79)
other constitutional aplastic anemia (284.09)
284.11  Antineoplastic chemotherapy induced pancytopenia
Excludes: aplastic anemia due to antineoplastic chemotherapy (284.89)
284.12  Other drug-induced pancytopenia
Excludes: aplastic anemia due to drugs (284.89)
284.19  Other pancytopenia
284.2    Myelophthisis
Leukoerythroblastic anemia
Myelophthisic anemia
Code firstthe underlying disorder, such as:
malignant neoplasm of breast (174.0-174.9, 175.0-175.9)
tuberculosis (015.0-015.9)
Excludes: idiopathic myelofibrosis (238.76)
myelofibrosis NOS (289.83)
myelofibrosis with myeloid metaplasia (238.76)
primary myelofibrosis (238.76)
secondary myelofibrosis (289.83)
284.8    Other specified aplastic anemias
284.81  Red cell aplasia (acquired) (adult) (with thymoma)
Red cell aplasia NOS
284.89  Other specified aplastic anemias
Aplastic anemia (due to):
chronic systemic disease
drugs
infection
radiation
toxic (paralytic)
Use additional E code to identify cause
284.9    Aplastic anemia, unspecified
Anemia:
aplastic (idiopathic) NOS
aregenerative
hypoplastic NOS
nonregenerative
Medullary hypoplasia
Excludes: refractory anemia (238.72)
285       Other and unspecified anemias
285.0    Sideroblastic anemia
Anemia:
hypochromic with iron loading
sideroachrestic
sideroblastic:
acquired
congenital
hereditary
primary
secondary (drug-induced) (due to disease)
sex-linked hypochromic
vitamin B6-responsive
Pyridoxine-responsive (hypochromic) anemia
Excludes: refractory sideroblastic anemia (238.72)
Use additional E code to identify cause, if drug-induced
285.1    Acute posthemorrhagic anemia
Anemia due to acute blood loss
Excludes: anemia due to chronic blood loss (280.0)
blood loss anemia NOS (280.0)
285.2    Anemia of chronic disease
Anemia in (due to) (with) chronic illness
285.21  Anemia in chronic kidney disease
Anemia in end-stage renal disease
Erythropoietin-resistant anemia (EPO resistant anemia)
285.22  Anemia in neoplastic disease
Excludes: anemia due to antineoplastic chemotherapy (285.3)
aplastic anemia due to antineoplastic chemotherapy (284.89)
285.29  Anemia of other chronic disease
Anemia in other chronic illness
285.3    Antineoplastic chemotherapy induced anemia
Anemia due to antineoplastic chemotherapy
Excludes: anemia due to drug NEC - code to type of anemia
anemia in neoplastic disease (285.22)
aplastic anemia due to antineoplastic chemotherapy (284.89)
285.8    Other specified anemias
Anemia:
dyserythropoietic (congenital)
dyshematopoietic (congenital)
von Jaksch's
Infantile pseudoleukemia
285.9    Anemia, unspecified
Anemia:
NOS
essential
normocytic, not due to blood loss
profound
progressive
secondary
Oligocythemia
Excludes: anemia (due to):
blood loss:
acute (285.1)
chronic or unspecified (280.0)
iron deficiency (280.0-280.9)
286       Coagulation defects
286.0    Congenital factor VIII disorder
Antihemophilic globulin [AHG] deficiency
Factor VIII (functional) deficiency
Hemophilia:
NOS
A
classical
familial
hereditary
Subhemophilia
Excludes: factor VIII deficiency with vascular defect (286.4)
286.1    Congenital factor IX disorder
Christmas disease
Deficiency:
factor IX (functional)
plasma thromboplastin component [PTC]
Hemophilia B
286.2    Congenital factor XI deficiency
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
286.3    Congenital deficiency of other clotting factors
Congenital afibrinogenemia
Deficiency:
AC globulin
factor:
I [fibrinogen]
II [prothrombin]
V [labile]
VII [stable]
X [Stuart-Prower]
XII [Hageman]
XIII [fibrin stabilizing]
Laki-Lorand factor
proaccelerin
Disease:
Owren's
Stuart-Prower
Dysfibrinogenemia (congenital)
Dysprothrombinemia (constitutional)
Hypoproconvertinemia
Hypoprothrombinemia (hereditary)
Parahemophilia
286.4    von Willebrand's disease
Angiohemophilia (A) (B)
Constitutional thrombopathy
Factor VIII deficiency with vascular defect
Pseudohemophilia type B
Vascular hemophilia
von Willebrand's (-Jürgens') disease
Excludes: factor VIII deficiency:
NOS (286.0)
with functional defect (286.0)
hereditary capillary fragility (287.8)
286.5    Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
286.52  Acquired hemophilia
Autoimmune hemophilia
Autoimmune inhibitors to clotting factors
Secondary hemophilia
286.53  Antiphospholipid antibody with hemorrhagic disorder
Lupus anticoagulant (LAC) with hemorrhagic disorder
Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder
Excludes: antiphospholipid antibody, finding without diagnosis (795.79)
antiphospholipid antibody syndrome (289.81)
antiphospholipid antibody with hypercoagulable state (289.81)
lupus anticoagulant (LAC) finding without diagnosis (795.79)
lupus anticoagulant (LAC) with hypercoagulable state (289.81)
systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (795.79)
systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (289.81)
286.59  Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
Antithrombinemia
Antithromboplastinemia
Antithromboplastinogenemia
Increase in:
anti-II (prothrombin)
anti-VIIIa
anti-IXa
anti-Xla
286.6    Defibrination syndrome
Afibrinogenemia, acquired
Consumption coagulopathy
Diffuse or disseminated intravascular coagulation [DIC syndrome]
Fibrinolytic hemorrhage, acquired
Hemorrhagic fibrinogenolysis
Pathologic fibrinolysis
Purpura:
fibrinolytic
fulminans
Excludes: that complicating:
abortion (634-638 with.1, 639.1)
pregnancy or the puerperium (641.3, 666.3)
disseminated intravascular coagulation in newborn (776.2)
286.7    Acquired coagulation factor deficiency
Deficiency of coagulation factor due to:
liver disease
vitamin K deficiency
Hypoprothrombinemia, acquired
Excludes: vitamin K deficiency of newborn (776.0)
Use additional E-code to identify cause, if drug-induced
286.9    Other and unspecified coagulation defects
Defective coagulation NOS
Deficiency, coagulation factor NOS
Delay, coagulation
Disorder:
coagulation
hemostasis
Excludes: abnormal coagulation profile (790.92)
hemorrhagic disease of newborn (776.0)
that complicating:
abortion (634-638 with.1, 639.1)
pregnancy or the puerperium (641.3, 666.3)
287       Purpura and other hemorrhagic conditions
Excludes:    hemorrhagic thrombocythemia (238.79)
purpura fulminans (286.6)
287.0    Allergic purpura
Peliosis rheumatica
Purpura:
anaphylactoid
autoimmune
Henoch's
nonthrombocytopenic:
hemorrhagic
idiopathic
rheumatica
Schönlein-Henoch
vascular
Vasculitis, allergic
Excludes: hemorrhagic purpura (287.39)
purpura annularis telangiectodes (709.1)
287.1    Qualitative platelet defects
Thrombasthenia (hemorrhagic) (hereditary)
Thrombocytasthenia
Thrombocytopathy (dystrophic)
Thrombopathy (Bernard-Soulier)
Excludes: von Willebrand's disease (286.4)
287.2    Other nonthrombocytopenic purpuras
Purpura:
NOS
senile
simplex
287.3    Primary thrombocytopenia
Excludes: thrombotic thrombocytopenic purpura (446.6)
transient thrombocytopenia of newborn (776.1)
287.30  Primary thrombocytopenia unspecified
Megakaryocytic hypoplasia
287.31  Immune thrombocytopenic purpura
Idiopathic thrombocytopenic purpura
Tidal platelet dysgenesis
287.32  Evans' syndrome
287.33  Congenital and hereditary thrombocytopenic purpura
Congenital and hereditary thrombocytopenia
Thrombocytopenia with absent radii (TAR) syndrome
Excludes: Wiskott-Aldrich syndrome (279.12)
287.39  Other primary thrombocytopenia
287.4    Secondary thrombocytopenia
Use additional E code to identify cause
Excludes: heparin-induced thrombocytopenia (HIT) (289.84)
transient thrombocytopenia of newborn (776.1)
287.41  Posttransfusion purpura
Posttransfusion purpura from whole blood (fresh) or blood products
PTP
287.49  Other secondary thrombocytopenia
Thrombocytopenia (due to):
dilutional
drugs
extracorporeal circulation of blood
massive blood transfusion
platelet alloimmunization
secondary NOS
287.5    Thrombocytopenia, unspecified
287.8    Other specified hemorrhagic conditions
Capillary fragility (hereditary)
Vascular pseudohemophilia
287.9    Unspecified hemorrhagic conditions
Hemorrhagic diathesis (familial)
288       Diseases of white blood cells
Excludes:    leukemia (204.0-208.9)
288.0    Neutropenia
Decreased Absolute Neutrophil Count (ANC)
Use additional code for any associated:
fever (780.61)
mucositis (478.11, 528.00-528.09, 538, 616.81)
Excludes: neutropenic splenomegaly (289.53)
transitory neonatal neutropenia (776.7)
288.00  Neutropenia, unspecified
288.01  Congenital neutropenia
Congenital agranulocytosis
Infantile genetic agranulocytosis
Kostmann's syndrome
288.02  Cyclic neutropenia
Cyclic hematopoiesis
Periodic neutropenia
288.03  Drug induced neutropenia
Use additional E code to identify drug
288.04  Neutropenia due to infection
288.09  Other neutropenia
Agranulocytosis
Neutropenia:
immune
toxic
288.1    Functional disorders of polymorphonuclear neutrophils
Chronic (childhood) granulomatous disease
Congenital dysphagocytosis
Job's syndrome
Lipochrome histiocytosis (familial)
Progressive septic granulomatosis
288.2    Genetic anomalies of leukocytes
Anomaly (granulation) (granulocyte) or syndrome:
Alder's (-Reilly)
Chédiak-Steinbrinck (-Higashi)
Jordan's
May-Hegglin
Pelger-Huet
Hereditary:
hypersegmentation
hyposegmentation
leukomelanopathy
288.3    Eosinophilia
Eosinophilia
allergic
hereditary
idiopathic
secondary
Eosinophilic leukocytosis
Excludes: Löffler's syndrome (518.3)
pulmonary eosinophilia (518.3)
288.4    Hemophagocytic syndromes
Familial hemophagocytic lymphohistiocytosis
Familial hemophagocytic reticulosis
Hemophagocytic syndrome, infection-associated
Histiocytic syndromes
Macrophage activation syndrome
288.5    Decreased white blood cell count
Excludes: neutropenia (288.01-288.09)
288.50  Leukocytopenia, unspecified
Decreased leukocytes, unspecified
Decreased white blood cell count, unspecified
Leukopenia NOS
288.51  Lymphocytopenia
Decreased lymphocytes
288.59  Other decreased white blood cell count
Basophilic leukopenia
Eosinophilic leukopenia
Monocytopenia
Plasmacytopenia
288.6    Elevated white blood cell count
Excludes: eosinophilia (288.3)
288.60  Leukocytosis, unspecified
Elevated leukocytes, unspecified
Elevated white blood cell count, unspecified
288.61  Lymphocytosis (symptomatic)
Elevated lymphocytes
288.62  Leukemoid reaction
Basophilic leukemoid reaction
Lymphocytic leukemoid reaction
Monocytic leukemoid reaction
Myelocytic leukemoid reaction
Neutrophilic leukemoid reaction
288.63  Monocytosis (symptomatic)
Excludes: infectious mononucleosis (075)
288.64  Plasmacytosis
288.65  Basophilia
288.66  Bandemia
Bandemia without diagnosis of specific infection
Excludes: confirmed infection - code to infection
leukemia  (204.00-208.9)
288.69  Other elevated white blood cell count
288.8    Other specified disease of white blood cells
Excludes: decreased white blood cell counts (288.50-288.59)
elevated white blood cell counts (288.60-288.69)
immunity disorders (279.0-279.9)
288.9    Unspecified disease of white blood cells
289       Other diseases of blood and blood-forming organs
289.0    Polycythemia, secondary
High-oxygen-affinity hemoglobin
Polycythemia:
acquired
benign
due to:
fall in plasma volume
high altitude
emotional
erythropoietin
hypoxemic
nephrogenous
relative
spurious
stress
Excludes: polycythemia:
neonatal (776.4)
primary (238.4)
vera (238.4)
289.1    Chronic lymphadenitis
Chronic:
adenitis any lymph node, except mesenteric
lymphadenitis any lymph node, except mesenteric
Excludes: acute lymphadenitis (683)
mesenteric (289.2)
enlarged glands NOS (785.6)
289.2    Nonspecific mesenteric lymphadenitis
Mesenteric lymphadenitis (acute) (chronic)
289.3    Lymphadenitis, unspecified, except mesenteric
289.4    Hypersplenism
"Big spleen" syndrome
Dyssplenism
Hypersplenia
Excludes: primary splenic neutropenia (289.53)
289.5    Other diseases of spleen
289.50  Disease of spleen, unspecified
289.51  Chronic congestive splenomegaly
289.52  Splenic sequestration
Code firstsickle-cell disease in crisis (282.42, 282.62, 282.64, 282.69)
289.53  Neutropenic splenomegaly
289.59  Other
Lien migrans
Perisplenitis
Splenic:
abscess
atrophy
cyst
fibrosis
infarction
rupture, nontraumatic
Splenitis
Wandering spleen
Excludes: bilharzial splenic fibrosis (120.0-120.9)
hepatolienal fibrosis (571.5)
splenomegaly NOS (789.2)
289.6    Familial polycythemia
Familial:
benign polycythemia
erythrocytosis
289.7    Methemoglobinemia
Congenital NADH [DPNH]-methemoglobin-reductase deficiency
Hemoglobin M [Hb-M] disease
Methemoglobinemia:
NOS
acquired (with sulfhemoglobinemia)
hereditary
toxic
Stokvis' disease
Sulfhemoglobinemia
Use additional E code to identify cause
289.8    Other specified diseases of blood and blood-forming organs
289.81  Primary hypercoagulable state
Activated protein C resistance
Antiphospholipid antibody syndrome
Antithrombin III deficiency
Factor V Leiden mutation
Lupus anticoagulant with hypercoagulable state
Protein C deficiency
Protein S deficiency
Prothrombin gene mutation
Systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state
Excludes: anti-phospholipid antibody, finding without diagnosis (795.79)
anti-phospholipid antibody with hemorrhagic disorder (286.53)
lupus anticoagulant (LAC) finding without diagnosis (795.79)
lupus anticoagulant (LAC) with hemorrhagic disorder (286.53)
secondary activated protein C resistance (289.82)
secondary antiphospholipid antibody syndrome (289.82)
secondary lupus anticoagulant with hypercoagulable state (289.82)
secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (289.82)
systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (795.79)
systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (286.53)
289.82  Secondary hypercoagulable state
Excludes: heparin-induced thrombocytopenia (HIT) (289.84)
289.83  Myelofibrosis
Myelofibrosis NOS
Secondary myelofibrosis
Code first the underlying disorder, such as:
malignant neoplasm of breast (174.0-174.9, 175.0-175.9)
Use additional code for associated therapy-related myelodysplastic syndrome, if applicable (238.72, 238.73)
Use additional external cause code if due to anti-neoplastic chemotherapy (E933.1)
Excludes: idiopathic myelofibrosis (238.76)
leukoerythroblastic anemia (284.2)
myelofibrosis with myeloid metaplasia (238.76)
myelophthisic anemia (284.2)
myelophthisis (284.2)
primary myelofibrosis (238.76)
289.84  Heparin-induced thrombocytopenia (HIT)
289.89  Other specified diseases of blood and blood-forming organs
Hypergammaglobulinemia
Pseudocholinesterase deficiency
289.9    Unspecified diseases of blood and blood-forming organs
Blood dyscrasia NOS
Erythroid hyperplasia

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