Other Metabolic And Immunity Disorders ICD 9 Codes (270-279)


OTHER METABOLIC AND IMMUNITY DISORDERS (ICD 9 CODES: 270-279)
Use additional code to identify any associated intellectual disabilities
270       Disorders of amino-acid transport and metabolism
Excludes:    abnormal findings without manifest disease (790.0-796.9)
disorders of purine and pyrimidine metabolism (277.1-277.2)
gout (274.00-274.9)
270.0    Disturbances of amino-acid transport
Cystinosis
Cystinuria
Fanconi (-de Toni) (-Debré) syndrome
Glycinuria (renal)
Hartnup disease
270.1    Phenylketonuria [PKU]
Hyperphenylalaninemia
270.2    Other disturbances of aromatic amino-acid metabolism
Albinism
Alkaptonuria
Alkaptonuric ochronosis
Disturbances of metabolism of tyrosine and tryptophan
Homogentisic acid defects
Hydroxykynureninuria
Hypertyrosinemia
Indicanuria
Kynureninase defects
Oasthouse urine disease
Ochronosis
Tyrosinosis
Tyrosinuria
Waardenburg syndrome
Excludes: vitamin B6-deficiency syndrome (266.1)
270.3    Disturbances of branched-chain amino-acid metabolism
Disturbances of metabolism of leucine, isoleucine, and valine
Hypervalinemia
Intermittent branched-chain ketonuria
Leucine-induced hypoglycemia
Leucinosis
Maple syrup urine disease
270.4    Disturbances of sulphur-bearing amino-acid metabolism
Cystathioninemia
Cystathioninuria
Disturbances of metabolism of methionine, homocystine, and cystathionine
Homocystinuria
Hypermethioninemia
Methioninemia
270.5    Disturbances of histidine metabolism
Carnosinemia
Histidinemia
Hyperhistidinemia
Imidazole aminoaciduria
270.6    Disorders of urea cycle metabolism
Argininosuccinic aciduria
Citrullinemia
Disorders of metabolism of ornithine, citrulline, argininosuccinic acid, arginine, and ammonia
Hyperammonemia
Hyperornithinemia
270.7    Other disturbances of straight-chain amino-acid metabolism
Glucoglycinuria
Glycinemia (with methylmalonic acidemia)
Hyperglycinemia
Hyperlysinemia
Pipecolic acidemia
Saccharopinuria
Other disturbances of metabolism of glycine, threonine, serine, glutamine, and lysine
270.8    Other specified disorders of amino-acid metabolism
Alaninemia
Ethanolaminuria
Glycoprolinuria
Hydroxyprolinemia
Hyperprolinemia
Iminoacidopathy
Prolinemia
Prolinuria
Sarcosinemia
270.9    Unspecified disorder of amino-acid metabolism
271       Disorders of carbohydrate transport and metabolism
Excludes:    abnormality of secretion of glucagon (251.4)
diabetes mellitus (249.0-249.9, 250.0-250.9)
hypoglycemia NOS (251.2)
mucopolysaccharidosis (277.5)
271.0    Glycogenosis
Amylopectinosis
Glucose-6-phosphatase deficiency
Glycogen storage disease
McArdle's disease
Pompe's disease
von Gierke's disease
271.1    Galactosemia
Galactose-1-phosphate uridyl transferase deficiency
Galactosuria
271.2    Hereditary fructose intolerance
Essential benign fructosuria
Fructosemia
271.3    Intestinal disaccharidase deficiencies and disaccharide malabsorption
Intolerance or malabsorption (congenital) (of):
glucose-galactose
lactose
sucrose-isomaltose
271.4    Renal glycosuria
Renal diabetes
271.8    Other specified disorders of carbohydrate transport and metabolism
Essential benign pentosuria
Fucosidosis
Glycolic aciduria
Hyperoxaluria (primary)
Mannosidosis
Oxalosis
Xylosuria
Xylulosuria
271.9    Unspecified disorder of carbohydrate transport and metabolism
272       Disorders of lipoid metabolism
Excludes:    localized cerebral lipidoses (330.1)
272.0    Pure hypercholesterolemia
Familial hypercholesterolemia
Fredrickson Type IIa hyperlipoproteinemia
Hyperbetalipoproteinemia
Hyperlipidemia, Group A
Low-density-lipoid-type [LDL] hyperlipoproteinemia
272.1    Pure hyperglyceridemia
Endogenous hyperglyceridemia
Fredrickson Type IV hyperlipoproteinemia
Hyperlipidemia, Group B
Hyperprebetalipoproteinemia
Hypertriglyceridemia, essential
Very-low-density-lipoid-type [VLDL] hyperlipoproteinemia
272.2    Mixed hyperlipidemia
Broad- or floating-betalipoproteinemia
Combined hyperlipidemia
Elevated cholesterol with elevated triglycerides NEC
Fredrickson Type IIb or III hyperlipoproteinemia
Hypercholesterolemia with endogenous hyperglyceridemia
Hyperbetalipoproteinemia with prebetalipoproteinemia
Tubo-eruptive xanthoma
Xanthoma tuberosum
272.3    Hyperchylomicronemia
Bürger-Grütz syndrome
Fredrickson type I or V hyperlipoproteinemia
Hyperlipidemia, Group D
Mixed hyperglyceridemia
272.4    Other and unspecified hyperlipidemia
Alpha-lipoproteinemia
Hyperlipidemia NOS
Hyperlipoproteinemia NOS
272.5    Lipoprotein deficiencies
Abetalipoproteinemia
Bassen-Kornzweig syndrome
High-density lipoid deficiency
Hypoalphalipoproteinemia
Hypobetalipoproteinemia (familial)
272.6    Lipodystrophy
Barraquer-Simons disease
Progressive lipodystrophy
Use additional E code to identify cause, if iatrogenic
Excludes: intestinal lipodystrophy (040.2)
272.7    Lipidoses
Chemically induced lipidosis
Disease:
Anderson's
Fabry's
Gaucher's
I cell [mucolipidosis I]
lipoid storage NOS
Niemann-Pick
pseudo-Hurler's or mucolipidosis III
triglyceride storage, Type I or II
Wolman's or triglyceride storage, Type III
Mucolipidosis II
Primary familial xanthomatosis
Excludes: cerebral lipidoses (330.1)
Tay-Sachs disease (330.1)
272.8    Other disorders of lipoid metabolism
Hoffa's disease or liposynovitis prepatellaris
Launois-Bensaude's lipomatosis
Lipoid dermatoarthritis
272.9    Unspecified disorder of lipoid metabolism
273       Disorders of plasma protein metabolism
Excludes:    agammaglobulinemia and hypogammaglobulinemia (279.0-279.2)
coagulation defects (286.0-286.9)
hereditary hemolytic anemias (282.0-282.9)
273.0    Polyclonal hypergammaglobulinemia
Hypergammaglobulinemic purpura:
benign primary
Waldenström's
273.1    Monoclonal paraproteinemia
Benign monoclonal hypergammaglobulinemia [BMH]
Monoclonal gammopathy:
NOS
associated with lymphoplasmacytic dyscrasias
benign
Paraproteinemia:
benign (familial)
secondary to malignant or inflammatory disease
273.2    Other paraproteinemias
Cryoglobulinemic:
purpura
vasculitis
Mixed cryoglobulinemia
273.3    Macroglobulinemia
Macroglobulinemia (idiopathic) (primary)
Waldenström's macroglobulinemia
273.4    Alpha-1-antitrypsin deficiency
AAT deficiency
273.8    Other disorders of plasma protein metabolism
Abnormality of transport protein
Bisalbuminemia
273.9    Unspecified disorder of plasma protein metabolism
274       Gout
Excludes:    lead gout (984.0-984.9)
274.0    Gouty arthropathy
274.00  Gouty arthropathy, unspecified
274.01  Acute gouty arthropathy
Acute gout
Gout attack
Gout flare
Podagra
274.02  Chronic gouty arthropathy without mention of tophus (tophi)
Chronic gout
274.03  Chronic gouty arthropathy with tophus (tophi)
Chronic tophaceous gout
Gout with tophi NOS
274.1    Gouty nephropathy
274.10  Gouty nephropathy, unspecified
274.11  Uric acid nephrolithiasis
274.19  Other
274.8    Gout with other specified manifestations
274.81  Gouty tophi of ear
274.82  Gouty tophi of other sites
Gouty tophi of heart
Excludes: gout with tophi NOS (274.03)
gouty arthropathy with tophi (274.03)
274.89  Other
Use additional code to identify manifestations, as:
gouty:
iritis (364.11)
neuritis (357.4)
274.9    Gout, unspecified
275       Disorders of mineral metabolism
Excludes:    abnormal findings without manifest disease (790.0-796.9)
275.0    Disorders of iron metabolism
Excludes: anemia:
iron deficiency (280.0-280.9)
sideroblastic (285.0)
275.01  Hereditary hemochromatosis
Bronzed diabetes
Pigmentary cirrhosis (of liver)
Primary (hereditary) hemochromatosis
275.02  Hemochromatosis due to repeated red blood cell transfusions
Iron overload due to repeated red blood cell transfusions
Transfusion (red blood cell) associated hemochromatosis
275.03  Other hemochromatosis
Hemochromatosis NOS
275.09  Other disorders of iron metabolism
275.1    Disorders of copper metabolism
Hepatolenticular degeneration
Wilson's disease
275.2    Disorders of magnesium metabolism
Hypermagnesemia
Hypomagnesemia
275.3    Disorders of phosphorus metabolism
Familial hypophosphatemia
Hypophosphatasia
Vitamin D-resistant:
osteomalacia
rickets
275.4    Disorders of calcium metabolism
Excludes: hungry bone syndrome (275.5)
parathyroid disorders (252.00-252.9)
vitamin D deficiency (268.0-268.9)
275.40  Unspecified disorder of calcium metabolism
275.41  Hypocalcemia
275.42  Hypercalcemia
275.49  Other disorders of calcium metabolism
Nephrocalcinosis
Pseudohypoparathyroidism
Pseudopseudohypoparathyroidism
275.5    Hungry bone syndrome
275.8    Other specified disorders of mineral metabolism
275.9    Unspecified disorder of mineral metabolism
276       Disorders of fluid, electrolyte, and acid-base balance
Excludes:    diabetes insipidus (253.5)
familial periodic paralysis (359.3)
276.0    Hyperosmolality and/or hypernatremia
Sodium [Na] excess
Sodium [Na] overload
276.1    Hyposmolality and/or hyponatremia
Sodium [Na] deficiency
276.2    Acidosis
Acidosis:
NOS
lactic
metabolic
respiratory
Excludes: diabetic acidosis (249.1, 250.1)
276.3    Alkalosis
Alkalosis:
NOS
metabolic
respiratory
276.4    Mixed acid-base balance disorder
Hypercapnia with mixed acid-base disorder
276.5    Volume depletion
Excludes: hypovolemic shock:
postoperative (998.09)
traumatic (958.4)
276.50  Volume depletion, unspecified
276.51  Dehydration
276.52  Hypovolemia
Depletion of volume of plasma
276.6    Fluid overload
Excludes: ascites (789.51-789.59)
localized edema (782.3)
276.61  Transfusion associated circulatory overload
Fluid overload due to transfusion (blood) (blood components)
TACO
276.69  Other fluid overload
Fluid retention
276.7    Hyperpotassemia
Hyperkalemia
Potassium [K]:
excess
intoxication
overload
276.8    Hypopotassemia
Hypokalemia
Potassium [K] deficiency
276.9    Electrolyte and fluid disorders not elsewhere classified
Electrolyte imbalance
Hyperchloremia
Hypochloremia
Excludes: electrolyte imbalance:
associated with hyperemesis gravidarum  (643.1)
complicating labor and delivery (669.0)
following abortion and ectopic or molar pregnancy (634-638 with.4, 639.4)
277       Other and unspecified disorders of metabolism
277.0    Cystic fibrosis
Fibrocystic disease of the pancreas
Mucoviscidosis
277.00  Without mention of meconium ileus
Cystic fibrosis NOS
277.01  With meconium ileus
Meconium:
ileus (of newborn)
obstruction of intestine in mucoviscidosis
277.02  With pulmonary manifestations
Cystic fibrosis with pulmonary exacerbation
Use additional code to identify any infectious organism present, such as:
pseudomonas (041.7)
277.03  With gastrointestinal manifestations
Excludes: with meconium ileus (277.01)
277.09  With other manifestations
277.1    Disorders of porphyrin metabolism
Hematoporphyria
Hematoporphyrinuria
Hereditary coproporphyria
Porphyria
Porphyrinuria
Protocoproporphyria
Protoporphyria
Pyrroloporphyria
277.2    Other disorders of purine and pyrimidine metabolism
Hypoxanthine-guanine-phosphoribosyltransferase deficiency [HG-PRT deficiency]
Lesch-Nyhan syndrome
Xanthinuria
Excludes: gout (274.00-274.9)
orotic aciduric anemia (281.4)
277.3    Amyloidosis
277.30  Amyloidosis, unspecified
Amyloidosis NOS
277.31  Familial Mediterranean fever
Benign paroxysmal peritonitis
Hereditary amyloid nephropathy
Periodic familial polyserositis
Recurrent polyserositis
277.39  Other amyloidosis
Hereditary cardiac amyloidosis
Inherited systemic amyloidosis
Neuropathic (Portuguese) (Swiss) amyloidosis
Secondary amyloidosis
277.4    Disorders of bilirubin excretion
Hyperbilirubinemia:
congenital
constitutional
Syndrome:
Crigler-Najjar
Dubin-Johnson
Gilbert's
Rotor's
Excludes: hyperbilirubinemias specific to the perinatal period (774.0-774.7)
277.5    Mucopolysaccharidosis
Gargoylism
Hunter's syndrome
Hurler's syndrome
Lipochondrodystrophy
Maroteaux-Lamy syndrome
Morquio-Brailsford disease
Osteochondrodystrophy
Sanfilippo's syndrome
Scheie's syndrome
277.6    Other deficiencies of circulating enzymes
Hereditary angioedema
277.7    Dysmetabolic syndrome X
Use additional code for associated manifestation, such as:
cardiovascular disease (414.00-414.07)
obesity (278.00-278.03)
277.8    Other specified disorders of metabolism
277.81  Primary carnitine deficiency
277.82  Carnitine deficiency due to inborn errors of metabolism
277.83  Iatrogenic carnitine deficiency
Carnitine deficiency due to:
Hemodialysis
Valproic acid therapy
277.84  Other secondary carnitine deficiency
277.85  Disorders of fatty acid oxidation
Carnitine palmitoyltransferase deficiencies (CPT1, CPT2)
Glutaric aciduria type II (type IIA, IIB, IIC)
Long chain 3-hydroxyacyl CoA dehydrogenase deficiency (LCHAD)
Long chain/very long chain acyl CoA dehydrogenase deficiency (LCAD, VLCAD)
Medium chain acyl CoA dehydrogenase deficiency (MCAD)
Short chain acyl CoA dehydrogenase deficiency (SCAD)
Excludes: primary carnitine deficiency (277.81)
277.86  Peroxisomal disorders
Adrenomyeloneuropathy
Neonatal adrenoleukodystrophy
Rhizomelic chrondrodysplasia punctata
X-linked adrenoleukodystrophy
Zellweger syndrome
Excludes: infantile Refsum disease (356.3)
277.87  Disorders of mitochondrial metabolism
Kearns-Sayre syndrome
Mitochondrial Encephalopathy, Lactic Acidosis and Stroke-like episodes  (MELAS syndrome)
Mitochondrial Neurogastrointestinal Encephalopathy syndrome (MNGIE)
Myoclonus with Epilepsy and with Ragged Red Fibers  (MERRF syndrome)
Neuropathy, Ataxia and Retinitis Pigmentosa  (NARP syndrome)
Use additional code for associated conditions
Excludes: disorders of pyruvate metabolism (271.8)
Leber's optic atrophy (377.16)
Leigh's subacute necrotizing encephalopathy (330.8)
Reye's syndrome (331.81)
277.88  Tumor lysis syndrome
Spontaneous tumor lysis syndrome
Tumor lysis syndrome following antineoplastic drug therapy
Use additional E code to identify cause, if drug-induced
277.89  Other specified disorders of metabolism
Hand-Schüller-Christian disease
Histiocytosis (acute) (chronic)
Histiocytosis X (chronic)
Excludes: histiocytosis:
acute differentiated progressive (202.5)
adult pulmonary Langerhans cell (516.5)
X, acute (progressive) (202.5)
277.9    Unspecified disorder of metabolism
Enzymopathy NOS
278       Overweight, obesity and other hyperalimentation
Excludes:    hyperalimentation NOS (783.6)
poisoning by vitamins NOS (963.5)
polyphagia (783.6)
278.0    Overweight and obesity
Excludes: adiposogenital dystrophy (253.8)
obesity of endocrine origin NOS (259.9)
Use additional code to identify Body Mass Index (BMI) if known (V85.0-V85.54)
278.00  Obesity, unspecified
Obesity NOS
278.01  Morbid obesity
Severe obesity
278.02  Overweight
278.03  Obesity hypoventilation syndrome
Pickwickian syndrome
278.1    Localized adiposity
Fat pad
278.2    Hypervitaminosis A
278.3    Hypercarotinemia
278.4    Hypervitaminosis D
278.8    Other hyperalimentation
279       Disorders involving the immune mechanism
Use additional code for associated manifestations
279.0    Deficiency of humoral immunity
279.00  Hypogammaglobulinemia, unspecified
Agammaglobulinemia NOS
279.01  Selective IgA immunodeficiency
279.02  Selective IgM immunodeficiency
279.03  Other selective immunoglobulin deficiencies
Selective deficiency of IgG
279.04  Congenital hypogammaglobulinemia
Agammaglobulinemia:
Bruton's type
X-linked
279.05  Immunodeficiency with increased IgM
Immunodeficiency with hyper-IgM:
autosomal recessive
X-linked
279.06  Common variable immunodeficiency
Dysgammaglobulinemia (acquired) (congenital) (primary)
Hypogammaglobulinemia:
acquired primary
congenital non-sex-linked
sporadic
279.09  Other
Transient hypogammaglobulinemia of infancy
279.1    Deficiency of cell-mediated immunity
279.10  Immunodeficiency with predominant T-cell defect, unspecified
279.11  DiGeorge's syndrome
Pharyngeal pouch syndrome
Thymic hypoplasia
279.12  Wiskott-Aldrich syndrome
279.13  Nezelof's syndrome
Cellular immunodeficiency with abnormal immunoglobulin deficiency
279.19  Other
Excludes: ataxia-telangiectasia (334.8)
279.2    Combined immunity deficiency
Agammaglobulinemia:
autosomal recessive
Swiss-type
X-linked recessive
Severe combined immunodeficiency [SCID]
Thymic:
alymphoplasia
aplasia or dysplasia with immunodeficiency
Excludes: thymic hypoplasia (279.11)
279.3    Unspecified immunity deficiency
279.4    Autoimmune disease, not elsewhere classified
Excludes: transplant failure or rejection (996.80-996.89)
279.41  Autoimmune lymphoproliferative syndrome
ALPS
279.49  Autoimmune disease, not elsewhere classified
Autoimmune disease NOS
279.5    Graft-versus-host disease
Code first underlying cause, such as:
complication of blood transfusion (999.89)
complication of transplanted organ (996.80-996.89)
Use additional code to identify associated manifestations, such as:
desquamative dermatitis (695.89)
diarrhea (787.91)
elevated bilirubin (782.4)
hair loss (704.09)
279.50  Graft-versus-host disease, unspecified
279.51  Acute graft-versus-host disease
279.52  Chronic graft-versus-host disease
279.53  Acute on chronic graft-versus-host disease
279.8    Other specified disorders involving the immune mechanism
Single complement [C1-C9] deficiency or dysfunction
279.9    Unspecified disorder of immune mechanism

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